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Warning-sign checks

Hirschsprung disease: when to get help

Go through these in order and stop at the first one that applies. If you are reading this for someone else, answer for them.

  1. 1

    Is any of this happening now?

    Call 911

    These concerns usually require timely clinical review but are not always emergencies.

    Fever with a swollen abdomen, explosive diarrhea, green vomiting, unusual sleepiness, or signs of serious illness needs urgent or emergency assessment because of the possibility of enterocolitis or obstruction.

    Other emergency signs, for anyone
    • Someone who is struggling to breathe, gasping, choking, or cannot get words out
    • Someone who has chest pain, tightness or pressure lasting more than a few minutes
    • Someone who has sudden weakness or drooping on one side of the face or body, slurred speech, or sudden confusion
    • Someone who is unconscious, or cannot be woken
    • Someone who is bleeding heavily and it will not stop with firm pressure
    • Someone who has had a seizure that will not stop, or does not wake up afterwards
    • Someone who has lips or skin that look pale, blue, grey or blotchy
    • Someone who you believe has taken an overdose or swallowed something poisonous
  2. 2

    Is any of this happening?

    Be seen today

    Contact the care team promptly for worsening constipation, repeated abdominal swelling, poor intake, vomiting, new stool leakage, painful bowel movements, or slowed growth.

  3. 3

    Does any of this apply?

    Book an appointment

    Regular follow-up with a pediatric surgeon is important after diagnosis and surgery.

    A pediatric gastroenterologist, dietitian, continence nurse, genetic counselor, or bowel-management team may also be involved.

    Routine visits may review stool frequency and consistency, abdominal swelling, continence, skin care, diet, growth, medicines, and any episodes of enterocolitis.

    Persistent symptoms should not automatically be assumed to be an expected result of surgery.

    They may need structured investigation.

    Follow-up should continue through adolescence.

    Young people benefit from learning the name of their operation, warning symptoms, current bowel plan, and how to obtain adult care.

    Some continue to need support for constipation, continence, sexual health, or emotional well-being after leaving pediatric services.

Every sign above is quoted from the sofidex article on Hirschsprung disease. If you are not sure, err upward — it is always reasonable to be checked.